Name must be less than 100 characters Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (CLIPPERS) is an uncommon and only recently described disorder characterized by infiltration of the brain by inflammatory cells. This can cause pain, swelling, inflammations, and in some cases, even ulceration and infection.

In this paper we report the case of a 52-year-old woman with multiple contrast enhancing lesions associated with a chronic lymphocytic inflammation of the infratentorial structures. May in some cases have other brainstem features or cognitive symptoms. Epub 2017 Jan 22.Brain Nerve. Feil A. L'absence et la diminuaton des vertebres cervicales (etude cliniqueet pathogenique); le syndrome dereduction numerique cervicales.

Other rare conditions which could present themselves in a similar way include neurosarcoidosis, paraneoplastic disease, infectious process (tuberculosis, neurosyphilis, Whipple’s disease, and parasitic infection), glioma, Behcet, Bickerstaff brainstem encephalitis and demyelinating diseases. The greatest issue with KTS syndrome is that the blood flow and/or lymph flow may be impeded, and will pool in the affected area. Around the holidays of 2011 he started to get double vision and then became very fatigued. Some people with KFS have no symptoms. Among older children and adults, The condition was first described by French physicians Klippel-Trenaunay syndrome: Spectrum and management Brain magnetic resonance imaging (MRI) of a patient with CLIPPERS (chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids) (coronar post-contrast T1-weighted images).
I was recently contacted by someone with a close relative who had been diagnosed with possible "SLIPPERS" syndrome. Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (CLIPPERS syndrome) is a chronic inflammatory disorder of the central nervous system of unknown etiology which was first described in 2010 by Pittock et al.

Common features may include a short neck, low hairline at the back of the head, and restricted movement of the upper spine. Wiley CLIPPERS is a recently described inflammatory brain disorder which produces a characteristic pattern of spots (lesions) seen in contrast-enhanced brain MRI. 2014;54(7):581-4. doi: 10.5692/clinicalneurol.54.581.Pittock SJ, Debruyne J, Krecke KN, Giannini C, van den Ameele J, De Herdt V, McKeon A, Fealey RD, Weinshenker BG, Aksamit AJ, Krueger BR, Shuster EA, Keegan BM.Brain. Specifically, it is a type of encephalomyelitis, which is a general term describing inflammation of the brain and spinal cord.

2016;100(1):20. MRI- 1. numerous nodular or punctate enhancing lesions bilaterally in at least 2 of 3: pons, cerebellum, brachium pontis 2. (c) Following oral glucocorticosteroids (GCS) and additive methotrexate therapy, a follow-up MRI performed 5 months later shows marked reduction in the extent of gadolinium enhancing lesions.

2019 Nov 4;19(1):266. doi: 10.1186/s12883-019-1507-z.Vola E, Russo C, Macera A, Del Vecchio W, Puoti G, Caranci F, Elefante A.Eur J Radiol Open. The three categories treated for types of spinal cord deficiencies are massive fusion of the cervical spine (Type I), the fusion of 1 or 2 vertebrae (Type II), and the presence of thoracic and lumbar spine anomalies in association with type I or type II Klippel–Feil syndrome (Type III). Clipboard, Search History, and several other advanced features are temporarily unavailable. Dr Bruno Di Muzio ◈ and Assoc Prof Frank Gaillard ◉ ◈ et al. Tani H, Nakajima H, Yamane K, Ohnishi H, Kimura F, Hanafusa T.Rinsho Shinkeigaku. DOI: Chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids (CLIPPERS) is a recently defined inflammatory central nervous system (CNS) disorder, prominently involving the brainstem and in particular the pons.

CLIPPERS has a basic entry at the NIH Office of Rare Diseases Research (this has been updated in 2013). Some patients initially diagnosed with CLIPPERS syndrome because of the typical clinical and radiological pattern later turned out to be an atypical manifestation of a primary central nervous system lymphoma [CSF analysis usually reveals an inconsistent pattern including mild pleocytosis, mild protein elevation and/or oligoclonal bands which, when serially assessed was often observed as a transient phenomenon [Certainly one of the most important criteria for the diagnosis of this disorder is the clinical as well as radiologic responsiveness to glucocorticosteroid (GCS) based immunosuppression [Clippers syndrome is a rare disorder and has only recently been described as a new disease entity in 2010 [The authors declare that they have no competing interests.Maenhoudt, W., Ramboer, K. and Maqueda, V., 2016. (Message moved into the forum by Bill Crum) Hi Tom, My husband who recently turned 61 was diagnosed with CLIPPERS syndrome in September of last year. “A Rare Cause of Dizziness and Gait Ataxia: CLIPPERS Syndrome”. We were concerned about the double vision and his eye dr. said that his eyes were fine. 2010 Sep;133(9):2626-34. doi: 10.1093/brain/awq164.

Maenhoudt, W., et al.. “A Rare Cause of Dizziness and Gait Ataxia: CLIPPERS Syndrome”.
Maenhoudt W, Ramboer K, Maqueda V. A Rare Cause of Dizziness and Gait Ataxia: CLIPPERS Syndrome. A specific serum or cerebrospinal fluid (CSF) biomarker for the disorder is currently not known.

Most countries seem to have some kind of organisation devoted to rare diseases. Unable to load your delegates due to an error Based on previous reports in literature - currently encompassing more than 50 reported cases of CLIPPERS - this review addresses clinical features, diagnostic criteria, differential diagnoses and therapeutic management of this peculiar disorder.


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